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Human disease Medical conditionGlycogen storage disease type IVOther namesAndersen's triad, Andersen’s disease[1]GlycogenSpecialtyEndocrinology, medical genetics, hepatology Glycogen storage disease type IV (GSD IV), or Andersen's Disease,[2][3] is a form of glycogen storage disease, which is caused by an inborn error of metabolism. It is the result of a mutation in the GBE1 gene, which causes a defect in the glycogen branching enzyme. Therefore, glycogen is not m…
French footballer (born 1949) Raymond Keruzoré Personal informationDate of birth (1949-06-17) 17 June 1949 (age 74)Place of birth Châteauneuf-du-Faou(Kastell-Nevez-ar-Faou), Brittany, FranceHeight 1.73 m (5 ft 8 in)Position(s) MidfielderYouth career Stade QuimpéroisSenior career*Years Team Apps (Gls)1969–1973 Rennes 88 (6)1973–1974 Marseille 25 (2)1974–1975 Rennes 19 (0)1975–1979 Laval 99 (14)1979–1981 Brest 38 (0)1981–1984 Guingamp 77 (5)International career19…
HangoutPoster filmSutradara Raditya Dika Produser Gope T Samtani Sunil Samtani Ditulis oleh Raditya Dika Pemeran Raditya Dika Prilly Latuconsina Soleh Solihun Titi Kamal Mathias Muchus Surya Saputra Dinda Kanya Dewi Gading Marten Bayu Skak Penata musikAndhika TriyadiSinematograferEnggar BudionoPenyuntingRyan PurwokoPerusahaanproduksiRapi FilmsTanggal rilis 22 Desember 2016 22 April 2017 (OIMF)Durasi110 MenitNegara IndonesiaBahasa Indonesia PendapatankotorRp 91,7 miliar Hangout adalah …
A precisão para a cronologia das peças de Shakespeare (como foram primeiramente escritas ou realizadas) é impossível de determinar, uma vez que não existem registros e muitas das obras foram encenadas muitos anos antes de serem publicadas. As primeiras versões impressas de várias peças de teatro de Shakespeare são edições piratas, mas muitas obras shakespearianas permaneceram inéditas até o aparecimento do First Folio (1623). Essa falta de informação, juntamente com outras discrep…
La iglesia de Santa María en el barrio de Putney, Londres, una iglesia de la tradición anglocatólica liberal, donde se llevó a cabo la reunión que condujo a la creación de la organización de iglesia inclusiva en 2003. Los términos anglocatolicismo liberal y anglocatólico liberal se refieren a personas, creencias y prácticas dentro del anglicanismo que afirman las perspectivas cristianas liberales mientras mantienen las tradiciones culturalmente asociadas con el anglocatolicismo. Descri…
Lamang tapaiSajianMakanan ringanTempat asal IndonesiaDibuat olehSuku MinangkabauBahan utamaLemang, beras ketan Lamang tapai adalah makanan ringan yang berasal dari Sumatera Barat, Indonesia. Rasanya manis, enak dan ada sedikit rasa fermentasi di dalamnya. Biasanya lamang tapai banyak dijumpai pada Idul Fitri, pernikahan, pesta adat atau acara khitanan. Namun, ada juga yang menjual lamang tapai sebagai hidangan berbuka puasa di bulan Ramadhan.[1] Ada dua cara makan lamang tapai. Pert…
Historic building in London, England Not to be confused with Lever House in New York City. Unilever HouseUnilever House seen from Blackfriars BridgeFormer namesLever HouseGeneral informationArchitectural styleNeoclassical Art DecoLocationBlackfriarsLondon, EC4United KingdomAddress100 Victoria EmbankmentCoordinates51°30′42″N 0°06′17″W / 51.511654°N 0.104671°W / 51.511654; -0.104671Current tenantsUnilever, Bristows, Royal MailConstruction started1929Completed193…
Naturschutzgebiet Halmberg IUCN-Kategorie IV – Habitat/Species Management Area Südhang der Bergkuppe mit typischer Vegetation, Blickrichtung Nordwest Südhang der Bergkuppe mit typischer Vegetation, Blickrichtung Nordwest Lage Hohenstein im Landkreis Reutlingen, Baden-Württemberg Fläche 10 ha Kennung 4.252 WDPA-ID 163504 Geographische Lage 48° 19′ N, 9° 19′ O48.3233333333339.3091666666667Koordinaten: 48° 19′ 24″ N, 9° 18′ …
Запрос «Top Spin» перенаправляется сюда; см. также другие значения. Силы прилагаемые к мячу при топ-спине (вращение совпадает с направлением движения)Эффект Магнуса у мяча с топ-спином: V — скорость, F — результирующая сила Топ-спин (от англ. Top Spin) — в видах спорта, в…
Fictional British school of magic from the Harry Potter universe Not to be confused with Hogwort. This article has multiple issues. Please help improve it or discuss these issues on the talk page. (Learn how and when to remove these template messages) This article needs additional citations for verification. Please help improve this article by adding citations to reliable sources. Unsourced material may be challenged and removed.Find sources: Hogwarts – news · newspapers…
Elaidinization is any chemical reaction which convert a cis- olefin to a trans- olefin in unsaturated fatty acids.[1][2] This is often performed on fats and oils to increase both the melting point and the shelf life without reducing the degree of unsaturation. The term originates from elaidic acid, the trans-isomer of oleic acid. Reaction Elaidinization of oleic acid, a common component of vegetable oils, yields its trans-isomer elaidic acid. Oleic acid Elaidic acid Oleic acid is…
2003 single by the Chemical Brothers For the concept from the fictional Dune universe, see Golden Path (Dune). The Golden PathSingle by the Chemical Brothers featuring the Flaming Lipsfrom the album Singles 93–03 B-sideNude NightReleased15 September 2003 (2003-09-15)Length4:47LabelFreestyle DustVirginAstralwerksSongwriter(s)Tom RowlandsEd SimonsWayne Michael CoyneSteven Gregory DrozdProducer(s)The Chemical BrothersThe Chemical Brothers singles chronology Come with Us/The Tes…
Indian political activist and poet (1879–1949) Sarojini Naidu1st Governor of United ProvincesIn office15 August 1947 – 2 March 1949Preceded byPosition establishedSucceeded byHormasji Peroshaw Mody44th President of the Indian National CongressIn office1925–1926Preceded byMahatma GandhiSucceeded byS. Srinivasa Iyengar Personal detailsBornSarojini Chattopadhyay(1879-02-13)13 February 1879Hyderabad, Hyderabad State, British Raj(present-day Telangana, India)Died2 March 1949(194…
Liaoning FC辽宁 Nome Liaoning Hongyun Football Club辽宁足球俱乐部宏运队 Alcunhas Tigres do Nordeste (东北虎)Liao-Zu (辽足) Fundação 1953 (70 anos) (amador) 1994 (29 anos) (profissional) Estádio Estádio Olímpico de Shenyang Capacidade 60,000 Localização Shenyang, Liaoning China Presidente Liu Chunheng Treinador(a) Yu Ming Material (d)esportivo Nike Competição China Super League Website [1] Uniformetitular Uniformealternativo Liaoning Hongyun Foot…
Đoàn chủ nhà ( Trung Quốc)Bảng huy chương Thế vận hội Mùa hè 2008HạngNOCVàngBạcĐồngTổng số1 Trung Quốc4822301002 Hoa Kỳ3639371123 Nga241323604 Anh Quốc191319515 Đức161114416 Úc141517467 Hàn Quốc13118328 Nhật Bản988259 Ý89102710 Pháp716204311 Hà Lan7541612 Ukraina74112213 Kenya6461614 Tây Ban Nha51131915 Jamaica5421116 Ba Lan4521117 Ethiopia4217…
Bandar Udara DaweiIATA: TVYICAO: VYDW TVYLokasi bandar udara di MyanmarInformasiJenisPublikPengelolaPemerintahMelayaniDawei, Myanmar (Burma)Ketinggian dpl26 mdplKoordinat14°06′13″N 098°12′13″E / 14.10361°N 98.20361°E / 14.10361; 98.20361Landasan pacu Arah Panjang Permukaan m kaki 16/34 2,135 7,005 Konsentrat Sumber:[1][2] Bandar Udara Dawei (IATA: TVY, ICAO: VYDW) adalah bandar udara yang melayani Dawei[1] (sebelumnya dik…
2009 video gameThe House of the Dead: OverkillWii box cover artDeveloper(s)Headstrong GamesModern Dream (Typing of the Dead)Publisher(s)SegaDirector(s)Steve PritchardTancred Dyke-WellsProducer(s)Bradley CrooksNeil McEwanDesigner(s)Alastair HalsbyProgrammer(s)Ian CrowtherArtist(s)Mark SlaterCasey FultonWriter(s)Jonathan BurroughsComposer(s)John SandersonNadeem DayaSeriesThe House of the DeadEngineBlitzTechPlatform(s)Wii, PlayStation 3, Microsoft Windows, iOS, AndroidReleaseWiiNA: February 10, 200…
Not to be confused with West London Free School. The London Free School (LFS) was founded on 8 March 1966, principally by John Hoppy Hopkins and Rhaune Laslett. Description The London Free School was a community action adult education project inspired by American free universities (and the Victorian Jewish Free School in Spitalfields). The organisers have been described as an anarchic temporary coalition of the old guard New Left and CND housing activists from the Rachman days and the new beatni…
Lambang Peta Data dasar Bundesland: Nordrhein-Westfalen Regierungsbezirk: Köln Ibu kota: Gummersbach Luas wilayah: 918,17 km² Penduduk: 290.225 (31 Mei 2005) Kepadatan penduduk: 316 jiwa per km² Pelat kendaraan bermotor: GM Pembagian administratif: 13 Gemeinden Alamatkantor bupati: Moltkestraße 4251643 Gummersbach Situs web resmi: www.oberbergischer-kreis.de Politik Bupati: Hagen Jobi (CDU) Peta Oberbergische Kreis adalah sebuah distrik (Landkreis) di Nordrhein-Westfalen, Jerman. lbsNordrhei…
Exponential Utility Function for different risk profiles In economics and finance, exponential utility is a specific form of the utility function, used in some contexts because of its convenience when risk (sometimes referred to as uncertainty) is present, in which case expected utility is maximized. Formally, exponential utility is given by: u ( c ) = { ( 1 − e − a c ) / a a ≠ 0 c a = 0 {\displaystyle u(c)={\begin{cases}(1-e^{-ac})/a&a\neq 0\\c&a=0\\\end{cases}}} c …