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Human disease Medical conditionGlycogen storage disease type IVOther namesAndersen's triad, Andersen’s disease[1]GlycogenSpecialtyEndocrinology, medical genetics, hepatology Glycogen storage disease type IV (GSD IV), or Andersen's Disease,[2][3] is a form of glycogen storage disease, which is caused by an inborn error of metabolism. It is the result of a mutation in the GBE1 gene, which causes a defect in the glycogen branching enzyme. Therefore, glycogen is no...
Eurovisiesongfestival 2017 Land Polen Nationale selectie Selectieproces Krajowe Eliminacje 2017 Datum 18 februari 2017 Artiest Kasia Moś Lied Flashlight Uitslag Halve finale 9de (119 punten) Finale 22ste (64 punten) Kasia Moś tijdens een repetitie in Kiev. Polen nam deel aan het Eurovisiesongfestival 2017 dat plaatsvond in Kiev, Oekraïne. Het was de 20ste deelname van het land aan het Eurovisiesongfestival. TVP was verantwoordelijk voor de Poolse bijdrage voor de editie van 2017. Sel...
Oskar Merikanto Données clés Nom de naissance Frans Oskar Mattsson Naissance 5 août 1868 Helsinki, Finlande Décès 17 février 1924 (à 55 ans) Hausjärvi, Finlande Activité principale Compositeur, pianiste, organiste, chef d'orchestre, pédagogue Descendants Aarre Merikanto modifier Oskar Merikanto ( audio) est un compositeur, pianiste, organiste, chef d'orchestre et pédagogue finlandais, né Frans Oskar Mattsson à Helsinki (Finlande) le 5 août 1868, décédé à Oitti — Hausj...
Волиця Коростенська дирекція Південно-Західна залізниця зупинний пункт Пост ЕЦРозташуванняРозташування Попільнянський районКоординати 50°02′28″ пн. ш. 29°40′48″ сх. д. / 50.04111° пн. ш. 29.68000° сх. д. / 50.04111; 29.68000СтруктураГлибина 0Платформ 1Істор...
Padi Reborn: Sang PenghiburGenreAcara varietasPresenterPadi Reborn Sahila Hisyam Adjis Doaibu Rigen Ridwan ReminNegara asalIndonesiaBahasa asliBahasa IndonesiaJmlh. musim2ProduksiLokasi produksiSound Stage NET., Graha Mitra, Karet Semanggi, Setiabudi, Jakarta SelatanDurasi60 menitRumah produksiNET. EntertainmentDistributorNet Mediatama TelevisiRilisJaringan asliNET.Format gambarHDTV (1080i 16:9)Format audioDolby Digital 5.1Rilis asli17 Juli 2020 (2020-07-17) –14 Maret 2021 (2...
North American theater of the War of the Spanish Succession (1702–13) Queen Anne's WarPart of the War of the Spanish Succession and the Indian WarsMap of European colonies in America, 1702Date8 March 1702 – 13 July 1713(13 years, 6 months and 4 weeks)LocationNorth AmericaResult British victory Treaty of Utrecht Treaty of Portsmouth (1713)Territorialchanges France cedes to Britain the control of Acadia, Newfoundland, Hudson Bay, and Saint KittsBelligerents France ...
Este artículo o sección tiene referencias, pero necesita más para complementar su verificabilidad.Este aviso fue puesto el 1 de noviembre de 2020. Para otros usos de este término, véase Julio César Rodríguez (desambiguación). Julio César Rodríguez Julio César Rodríguez en 2020Información personalNombre de nacimiento Julio César Rodríguez SierraApodo El JC que le dicenNacimiento 2 de julio de 1969 (54 años)Concepción, ChileResidencia Santiago de ChileNacionalidad ChilenaL...
Punai Burung betina Klasifikasi ilmiah Kerajaan: Animalia Filum: Chordata Kelas: Aves Ordo: Columbiformes Famili: Columbidae Genus: TreronVieillot, 1816 Punai (bahasa Inggris: Green Pigeon) adalah genus burung berukuran sedang hingga besar yang tergolong famili Columbidae dan bersaudara dekat dengan merpati. Punai termasuk burung arboreal yang beraktivitas di atas pohon, memamakan buah-buahan. Genus ini terdiri dari 23 spesies. Burung punai (bangsa: Columbiformes,suku: Columbidae) tersebar lu...
Politics of Norway Constitution Monarchy King Harald V Crown Prince Haakon Government Council of State (current cabinet) Prime Minister (list) Jonas Gahr Støre List of governments Parliament Storting President: Masud Gharahkhani Norwegian Parliamentary Ombudsman Political parties Politicians Recent elections Parliamentary: 2021201720132009 Local: 2023201920152011 Local government Administrative divisions Counties (Fylker) Municipalities (Kommuner) Sámi Parliament Foreign relations European ...
Doornstruweel in de Millingerwaard (Nederland) Een struweel, ook struikgewas genoemd, is een begroeiing die als formatie voorkomt waarin struiken dominant en aspectbepalend zijn. Doorgaans worden de struiken die een struweel domineren niet hoger dan ongeveer 5 meter. Een boomlaag is bij een struweel (per definitie) afwezig of slecht ontwikkeld. Ook dwergvormen van boomsoorten (bijvoorbeeld bij krummholz) kunnen een struweel domineren. Een struweel dat wordt gedomineerd door dwergstruiken word...
Not to be confused with William Carey University. William Carey International UniversityTypePrivateEstablished1977PresidentPaul Cornelius, PhDAcademic staff8 full-time (11 Field Personnel)Administrative staff12Postgraduates51 (2019)[1]LocationPasadena, California, United StatesColorsGreen and GoldWebsitewww.wciu.edu William Carey International University (WCIU) is a private faith-based university in Pasadena, California, USA, that provides distance education programs. WCIU offer...
Italian cultural and philosophical movement Statue of Cesare Beccaria, widely considered one of the greatest thinkers of the Age of Enlightenment. The Enlightenment in Italy (Italian: Illuminismo italiano) was a cultural and philosophical movement that began in the second half of the eighteenth century, characterized by the discussion of the epistemological, ethical, and political issues of the Enlightenment thought of the eighteenth century.[1][2][3] History In Italy ...
Charente Departament Herb Flaga Państwo Francja Region Nowa Akwitania Prefektura Angoulême Kod ISO 3166-2 FR-16 Powierzchnia 5 956 km² Populacja (2010[1])• liczba ludności 351 577 • gęstość 59 os./km² Szczegółowy podział administracyjny Liczba podprefektur 2 Liczba kantonów 35 Liczba gmin 404 Położenie na mapie Multimedia w Wikimedia Commons Informacje w Wikipodróżach Strona internetowa Charente (wymowaⓘ) – francuski departament położo...
Group of Latin American premium television networks Television channel Star PremiumBroadcast areaLatin AmericaHeadquartersAtlanta, Georgia (programming/playout)ProgrammingLanguage(s)English with subtitles in Spanish and PortuguesePicture format480p (SDTV) 1080i (HDTV)OwnershipOwner LAPTV (1997–2012) 21st Century Fox (2013–2018; under Fox International Channels Latin America) The Walt Disney Company (2019–2022; under The Walt Disney Company Latin America) HistoryLaunchedLatin America: Ju...
Esta página ou se(c)ção precisa ser formatada para o padrão wiki. Por favor ajude a formatar esta página de acordo com as diretrizes estabelecidas. (Outubro de 2023) Força Aérea dos Estados Unidos Emblema da Força Aérea dos Estados Unidos[1] País Estados Unidos Corporação Forças Armadas dos Estados UnidosDepartamento da Força Aérea Subordinação Departamento de Defesa dos Estados Unidos Denominação United States Air Force Sigla USAF Criação 1907 Aniversários 18 de setembr...
Blick über den Platz nach Nordosten mit Venusbrunnen Der Sloane Square ist ein Platz zwischen den Londoner Stadtteilen Knightsbridge, Belgravia und Chelsea. Der Platz ist Teil der Hans Town und wurde 1771 von Henry Holland entworfen. Die „Town“ und der Platz, wie auch eine Straße, wurden nach dem Mediziner Hans Sloane benannt.[1] Der Platz liegt an den Enden der bekannten Straßen Kings Road und Sloane Street. In den 1980er Jahren wurde der Spitzname Sloane Rangers für Sprößl...
American physicist David H. FrischDavid H. Frisch Los Alamos wartime security badge.Born(1918-03-12)March 12, 1918New York City, New YorkDiedMay 23, 1991(1991-05-23) (aged 73)NationalityAmericanEducationPrincetonKnown forHelped develop the atom bomb in World War IISpouseRose Epstein FrischAwardsFellow of the American Physical SocietyScientific careerFieldsPhysicsInstitutionsLos AlamosThesis (1947)Doctoral advisorVictor WeisskopfDoctoral studentsGeorge Smoot[1] David Hen...
Vanchi Bhumi വഞ്ചി ഭൂമിEnglish: The Lord of VanchiFlag of the Kingdom of TravancoreNational anthem of TravancoreLyricsUlloor S. Parameswara IyerAdopted1937Relinquished1947Audio sampleNational Anthem of Travancore sung by Kamala Krishnamurthy in 1937 played in Travancore Radio Stationfilehelp Vanchi Bhumi (alternatively Vanji Bhumi) was the national anthem of the erstwhile Kingdom of Travancore which now forms part of Kerala. It was formally known as the Vanchishamangala...
Moshi Moshi, Terumi DesuCover of Moshi Moshi, Terumi Desu volume 1 by Shogakukanもしもし、てるみです。GenreRomantic comedy[1] MangaWritten byEtsuko MizusawaPublished byShogakukanMagazineBig Comic SpiritsDemographicSeinenOriginal runMarch 2016 – February 2018Volumes2 Original net animationStudioProduction I.GReleasedJune 8, 2018 Moshi Moshi, Terumi Desu (もしもし、てるみです。, lit. Hello, This is Terumi) is a Japanese manga series by Etsuko Mizusawa. ...
34th chapter of the Qur'an Q34 redirects here. For the bus service, see Q34 (New York City bus). Sura 34 of the Quranسَبَأ Saba’ShebaArabic textEnglish translationClassificationMeccanPositionJuzʼ 22No. of Rukus6No. of verses54← Quran 33Quran 35 → Quran History Waḥy First revelation Asbab al-Nuzul Historicity Manuscripts Samarkand Kufic Quran Sanaa manuscript Topkapi manuscript Birmingham manuscript Divisions Surah List Meccan Medinan Āyah Juz' Muqatta'at Conte...