Worster-Drought syndrome

This article is about the form of cerebral palsy. For the type of dementia also known as Worster-Drought syndrome, see Familial British dementia.

Worster-Drought syndrome is a form of congenital suprabulbar paresis that occurs in some children with cerebral palsy. It is caused by inadequate development of the corticobulbar tracts and causes problems with the mouth and tongue including impaired swallowing.^[1] A similar syndrome in adults is called anterior opercular syndrome.^[1][2]

A 1986 study of a family in which multiple members had Worster-Drought syndrome suggested it might be hereditary.^[3]

A 2000 review of cases classified Worster-Drought Syndrome as a form of cerebral palsy, caused by early damage to the brain, but identified no obvious causes during gestation or birth and found some families with a history of the condition.^[4] The syndrome was named after Cecil Charles Worster-Drought, the doctor who described it in 1956.^{[citation needed]}

References

1. Suresh PA, Deepa C (September 2004). "Congenital suprabulbar palsy: a distinct clinical syndrome of heterogeneous aetiology". Developmental Medicine and Child Neurology. 46 (9): 617–25. doi:10.1111/j.1469-8749.2004.tb01026.x. PMID 15344522.
2. Christen HJ, Hanefeld F, Kruse E, Imhäuser S, Ernst JP, Finkenstaedt M (February 2000). "Foix-Chavany-Marie (anterior operculum) syndrome in childhood: a reappraisal of Worster-Drought syndrome". Developmental Medicine and Child Neurology. 42 (2): 122–32. doi:10.1017/S0012162200000232. PMID 10698330.
3. Patton MA, Baraitser M, Brett EM (February 1986). "A family with congenital suprabulbar paresis (Worster-Drought syndrome)". Clinical Genetics. 29 (2): 147–50. doi:10.1111/j.1399-0004.1986.tb01239.x. PMID 3955865. S2CID 20422659.
4. Clark M, Carr L, Reilly S, Neville BG (October 2000). "Worster-Drought syndrome, a mild tetraplegic perisylvian cerebral palsy. Review of 47 cases". Brain. 123 (10): 2160–70. doi:10.1093/brain/123.10.2160. PMID 11004132.

Sources

• Worster-Drought C (August 1956). "Congenital suprabulbar paresis". The Journal of Laryngology and Otology. 70 (8): 453–63. doi:10.1017/S0022215156000115. PMID 13357872.
• Malcolm Ray McNeil, Clinical Management of Sensorimotor Speech Disorders, New York: Thieme, 1997, p. 407.
• Bianca Specht-Moser, "Die Behandlung des Kausystems in der Kinder- und Jugendneurorehabilitation - Elemente eines Rehabilitationspfades" MS Thesis, Danube University Krems, September 2004 (pdf, German)